Congenital self-healing reticulohistiocytosis in a newborn: unusual oral and cutaneous manifestations

Abstract Background Congenital self-healing reticulohistiocytosis (CSHRH), also called Hashimoto-Pritzker disease, is a rare and benign variant of Langerhans cell histiocytosis, characterized by cutaneous lesions without extracutaneous involvement. Case presentation We present case CSHRH with diffuse skin erosions in the oral mucosa, since birth lasting for 2 months, we perform review literature on Pubmed last 10 years. Conclusions Our confirm that actually underestimated, may be patients CSHRH. Patients affected require close follow-up until first years life, due to unpredictable course order avoid missing diagnosis more aggressive types this disorder.